Sturge-Weber syndrome with extensive intracranial calcifications contralateral to the bulk of the facial nevus, normal intelligence, and absent seizure disorder.

Sturge-Weber syndrome is a rare condition first described by Sturge in 1879 in a case report of an epileptic patient [1] . The association of intracranial calcifications was subsequently described by Weber in 1922, giving this condition its familiar eponym [2] . The classical findings include gyriform intracranial calcifications, congenital and usually unilateral capillary facial nevus, convulsive disorder, glaucoma, some degree of mental deficiency, and hemiparesis and hemiatrophy.